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NHS
Giant Cell Arteritis — Clinical Decision Support
BSR 2020 Guideline

Always consider alternative diagnoses

Herpes zoster (shingles) Tension / cluster / migraine headache Trigeminal neuralgia Cervical spondylosis Acute angle closure glaucoma Retinal TIA / embolic visual deficits TMJ dysfunction Sinus disease / ear disease Intracranial pathology (haemorrhage, tumour)
Step 1 — Presenting features (patients almost always >50)

Select all features present. Visual and ischaemic features carry the highest urgency.

⚠ Sight-threatening / ischaemic

Acute visual loss
Transient or permanent, one or both eyes
Diplopia / double vision
New onset, attributed to GCA
Jaw or tongue claudication
Pain on chewing — high specificity for GCA
Visual disturbance
Colour change, blurring, field defect, amaurosis fugax

Cranial / vascular features

New onset headache
Typically temporal
Scalp tenderness
Including pain on brushing hair
Temporal artery abnormal
Tender, thickened, nodular, reduced pulsation
Neurological features
TIA, stroke, confusion, cognitive change

Systemic / PMR features

PMR features
Shoulder/hip girdle pain & stiffness
Constitutional symptoms
Malaise, fatigue, fever, weight loss, sweats
Already on steroids
Markers may be suppressed — see caveat
Step 2 — Inflammatory markers

⚠ Critical marker caveats — read before interpreting

Normal ESR does not exclude GCA. Up to 15% of biopsy-proven GCA cases have a normal ESR — and those patients carry the same risk of sight loss as those with elevated ESR (Myklebust & Gran, 1996).
Normal CRP does not exclude GCA. Approximately 10% of GCA patients have both normal ESR and normal CRP at diagnosis. CRP is the more sensitive single marker (sensitivity ~87% vs ~84% for ESR).
Plasma viscosity (PV) is the primary marker in NHS Grampian (replacing ESR routinely). PV is unaffected by anaemia or polycythaemia. However, PV and ESR each produce ~13% false negatives independently in biopsy-proven GCA — they are not always equivalent. If PV is normal but clinical suspicion remains high, CRP adds independent information.
ESR and CRP can be discordant — an elevated CRP with normal PV/ESR (or vice versa) does not reassure. Clinical features take precedence over any single marker.
Steroids suppress markers rapidly. If the patient is already on any corticosteroid, normal markers must not be used to downgrade suspicion. Clinical features dominate entirely.
Plasma viscosity (cP) Normal: <1.72 cP · Raised: ≥1.72 · Significantly raised: ≥1.90
Primary marker in NHS Grampian (BSR: use if ESR unavailable)
CRP (mg/L) Normal: <10 · Raised: 10–49 · Significantly raised: ≥50
Most sensitive single marker. Adequate response defined as CRP ≤10
ESR (mm/hr) Normal varies with age/sex · Significantly raised: ≥80 mm/hr
Normal ESR does not exclude GCA
Steroid effect flagged: Patient is already on corticosteroids. All inflammatory markers may be partially or fully suppressed. A normal result in this context cannot be used to downgrade clinical suspicion. Clinical features must carry full diagnostic weight.
All entered markers are within normal range. This does not exclude GCA. Up to 10% of biopsy-proven GCA cases have entirely normal inflammatory markers at diagnosis. If clinical features are present, proceed on clinical grounds and discuss with specialist without delay.

Step 3 — Select your clinical judgement to generate the action plan

BSR 2020 defines "strongly suspected GCA" as: "in the assessing clinician's judgement, GCA is a more likely explanation for the patient's symptoms than any other condition." No score replaces this gate — click the option that best reflects your clinical assessment.

Features recorded — click one of the options below to generate your action plan
🚨 Emergency — same calendar day
Acute sight-threatening GCA: immediate action required
  • 1Call Ophthalmology now. BSR 2020 strong recommendation: patients with new visual loss or diplopia must be seen by ophthalmology on the same calendar day.
  • 2Start Prednisolone 60mg orally immediately (NHS Grampian). Do not wait for blood results. If IV methylprednisolone is accessible, this is preferred for sight-threatening disease.
  • 3Consider gastric protection: Omeprazole 20mg daily unless contraindicated.
  • 4Bloods before or immediately after first dose: FBC, U+Es, CRP, Plasma Viscosity, LFTs. Do not delay treatment waiting for results.
  • 5Do not send this patient home without speaking to a specialist. GCA with visual symptoms is a medical emergency.
  • 6Document fully: all symptoms, signs, date/time of first steroid dose and clinical reasoning.
Out of hours: Rheumatology is unavailable. Ophthalmology on-call must be contacted via hospital switchboard. Start Prednisolone 60mg now. Document start date, start dose, and clinical rationale clearly. Refer to Rheumatology on the next working day.
⚡ Urgent — same working day
GCA strongly suspected — same-day specialist discussion required
  • 1Discuss with Rheumatology today. BSR 2020: patients should be evaluated by a specialist ideally on the same working day, and in all cases within 3 working days. Do not send home without this discussion.
  • 2Start Prednisolone 60mg orally if GCA is strongly suspected, before the specialist review. First dose can be given without waiting for blood results. Note date and dose in referral letter.
  • 3Consider gastric protection: Omeprazole 20mg daily unless contraindicated.
  • 4Bloods now: FBC, U+Es, CRP, Plasma Viscosity, LFTs. Take before or immediately after first steroid dose.
  • 5Bone prophylaxis if ≥65 years: start Calcium + Vitamin D immediately. Bisphosphonate immediately. DEXA scan will be considered by Rheumatology.
  • 6Safety net: advise patient to return immediately if any visual symptoms develop (blurring, visual loss, diplopia, colour change). This changes the pathway to emergency.
  • 7Document fully: all symptoms, signs, date/time of steroid dose and clinical reasoning. Include in referral.
Out of hours: Rheumatology is unavailable. Start Prednisolone 60mg now, document clearly, and ensure urgent same-day Rheumatology referral first thing on the next working day.
⚠ Possible GCA — do not discharge without plan
GCA possible — same-day specialist discussion still required
  • 1Even where uncertainty exists, do not send the patient home without specialist discussion if GCA remains in the differential. A telephone discussion with Rheumatology today is appropriate.
  • 2Bloods urgently: FBC, U+Es, CRP, Plasma Viscosity, LFTs. Remember: normal markers do not exclude GCA.
  • 3Await specialist advice before initiating steroids in this group — the decision requires specialist input given diagnostic uncertainty.
  • 4Safety net explicitly: advise patient to return immediately if jaw pain develops, any visual symptom arises, or headache worsens. This changes pathway to urgent/emergency.
  • 5Document uncertainty and safety-net advice in the records.
GCA not in differential
GCA excluded on clinical grounds — document and manage alternative diagnosis
  • 1Document clearly in the notes that GCA was considered and excluded, with reasoning.
  • 2Pursue alternative diagnoses actively — see differential list above.
  • 3Safety net: if new headache, jaw pain, visual symptoms, or scalp tenderness develop, patient should return promptly for reassessment.
  • 4In patients with known PMR: maintain a low threshold for reassessment — GCA can emerge during the PMR disease course.